Faciobrachio-crural dystonic seizures in LGI1 limbic encephalitis: A treatable cause of falls

نویسندگان

  • Fatme Seval Ismail
  • Stoyan Popkirov
  • Jörg Wellmer
  • Wenke Grönheit
چکیده

Faciobrachial dystonic seizures (FBDS) are closely associated with antibodies (Ab) to the leucine-rich glioma inactivated-1 protein (LGI1) component of the voltage-gated potassium channel (VGKC) complex. They precede or indicate the onset of limbic encephalitis (LE). Immunotherapy can prevent the development of LE and cognitive impairment. FBDS are very brief, very frequent unilateral dystonic seizure-like events that always affect the arm and commonly affect the ipsilateral face. Involvement of the leg is rare, and little has been reported on so-called faciobrachio-crural dystonic seizures (FBCDS), which are associated with falls as well. Hence, FCBDS are a rare but treatable differential diagnosis of recurrent falls.

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عنوان ژورنال:

دوره 2  شماره 

صفحات  -

تاریخ انتشار 2015